SUMMARY
When common infectious agents and other causes of fever such as neoplastic and rheumatologic diseases, immune deficiencies, various endocrinologic and metabolic disorders are differentiated, periodic fever syndromes must be brought in mind in recurrent fever attacks of childhood. Among periodic fever syndromes PFAPA, hyper-IgD syndrome, tumor necrosis factor receptor-associated periodic syndrome (TRAPS), familial cold urticaria, Muckle-Wells syndromes, familial Mediterranean fever and cyclic neutropenia are well described.  Although clinical findings are clear enough , as there is no specific test for these diseases, it is sometimes hard to diagnose.  Hereby, we rewieved these diseases which may cause recurrent fever attacks in children. (Güncel Pediatri 2007; 5: 57-61)
Key words: Cyclic neutropenia, familial cold urticaria, familial mediterenean fever, hyperIgD, Muckle-Wells, periodic fever, PFAPA, TRAPS